The term hemangioendothelioma has been used to designate various groups of vascular tumours.

There are four main recognised subgroups of these tumours:

• Epithelioid hemangioendothelioma (EHE), having epithelial-like cells lining the vascular channels
• Spindle cell hemangioendothlioma (SCH), has spindle cells separating the vessels.
• Kaposiform hemangioendothelioma (KHE) which is a locally invasive tumour, occuring in young children and having no capacity to metastasize
• Malignant endovascular papillary angioendothelioma, also known as a Dabska tumour, a. low-grade angiosarcoma that can affect the skin of children

Other forms of hemangioendotheliomas have recently been noted, eg, Retiform, Composite and Polymorphous.

Sometimes, it may be hard to make a correct distinction between these and other rare vascular conditions.

Hemangioendothelioma in the lung was originally described as Intravascular Bronchioloalveolar Tumour.

Please email info@HEARDsupport.org for more information.